The life expectancy with Wegener's granulomatosis is around 5 months without treatment and less than half of people with Wegener's granulomatosis survive one year without treatment.
With treatment the life expectancy with Wegener's granulomatosis is around 8 years and the 5 year survival rate is 74 to 79 percent.
The 1 year mortality rate of Wegener's granulomatosis is around 11 percent but can range from 2.2 percent to 25 percent depending on the severity of the disease and also the intensity of the treatment.
The most common cause of death in Wegener's granulomatosis is infection, kidney failure, respiratory failure, malignancy and cardiovascular events.
In most people, Wegener's granulomatosis affects the respiratory tract and the kidneys.
Some people with wegener's granulomatosis may have mild disease, while others develop life-threatening complications.
Wegener's granulomatosis can develop slowly over many months or it can develop rapidly over several days (acute).
Wegener's granulomatosis, which is now known as granulomatosis with polyangiitis, is a rare disease which causes inflammation of your blood vessels and the formation of granulomas.
Wegener's granulomatosis is one of a group of blood vessel disorders called vasculitis.
Wegener's granulomatosis is serous and can be fatal and prompt treatment is important.
In most cases, the exact cause of Wegener's granulomatosis is not known, but it is an autoimmune disorder.
Three mechanisms have also been described in the pathogenesis of central nervous system, spread of the granulomatous tissue from the nasal, paranasal or orbital cavity; the development of granulomas in the brain, meninges, cranial nerves or in parietal bone; and granulomatous vasculitis of the central nervous system.